As a result of the vestibular abnormalities, children with the condition have trouble with balance. This type of Usher syndrome also causes abnormalities of the vestibular system, which is the part of the inner ear that helps maintain the body's balance and orientation in space. Worsening vision loss caused by retinitis pigmentosa becomes apparent in childhood. The types are further divided into subtypes based on their genetic cause.\n\nMost individuals with Usher syndrome type I are born with severe to profound hearing loss. ![]() These types are distinguished by the severity of hearing loss, the presence or absence of balance problems, and the age at which signs and symptoms appear. However, many people with retinitis pigmentosa retain some central vision throughout their lives.\n\nResearchers have identified three major types of Usher syndrome, designated as types I, II, and III. In some cases, vision is further impaired by clouding of the lens of the eye (cataracts). Over time, these blind spots enlarge and merge to produce tunnel vision. Loss of night vision begins first, followed by blind spots that develop in the side (peripheral) vision. ![]() Vision loss occurs as the light-sensing cells of the retina gradually break down. ![]() The loss of vision is caused by an eye disease called retinitis pigmentosa (RP), which affects the layer of light-sensitive tissue at the back of the eye (the retina). The hearing loss is classified as sensorineural, which means that it is caused by abnormalities of the inner ear. Usher syndrome is a condition characterized by partial or total hearing loss and vision loss that worsens over time.
0 Comments
Leave a Reply. |
AuthorWrite something about yourself. No need to be fancy, just an overview. ArchivesCategories |